Scleroderma Types Localized Morphea Rare

Rare Types of Morphea

Bullous Morphea

Overview

Photo of Bullous Morphea. Bullous morphea is a rare disease, which occurs most commonly on the lower extremities and inferior abdomen. Fewer than 100 cases have been reported in the world literature. Dermatology Online Journal.

Bullous Morphea Case Reports

(Case Reports): Three cases of bullous morphea: histopathologic findings with implications regarding pathogenesis. All of our cases showed hemorrhagic content in the bullae, which suggests local trauma as a mechanism involved in bulla formation. PubMed, J Cutan Pathol.

(Case Report): Ulcers caused by bullous morphea treated with tissue-engineered skin. A patient with bullous morphea with long-standing ulcers was successfully treated with the tissue-engineered skin Apligraf. The patient experienced rapid improvement in granulation tissue and the ulcers healed 4 months after a single application. Int J Dermatol.

(Case Report): Bullous morphea is a rare disease, which occurs most commonly on the lower extremities and inferior abdomen. Fewer than 100 cases have been reported in the world literature. Multiple authors have concluded that morphea and bullous morphea are distinct manifestations of the same disease. Dermatology Online Journal.

(Case Report): Lichen sclerosus et atrophicus, bullous morphea, and systemic lupus erythematosus. Lichen sclerosus et atrophicus (LSA) rarely coexists with morphea, especially when bullae occur in lesions of morphea. Here we report the case of a 15-year-old girl with this condition, who also fulfilled four out of 11 diagnostic criteria for systemic lupus erythematosus (SLE). J Microbiol Immunol Infect. (Also see Lichen Sclerosus and Lupus)

Deep Morphea

Deep morphea is characterized by ill-defined, bound-down, sclerotic plaques with a cobblestone or pseudo-cellulite appearance. The groove sign (a depression along the course of a vein, between muscle groups, or both) may be evident later in the course of disease. Deep morphea lesions are frequently hyperpigmented, but, because of the deeper level of inflammation, they lack the other color changes typical of plaque-type morphea. Distribution of lesions is often symmetric. Medscape.

Dermatitis Artefacta or Factitial Dermatitis

Dermatitis artefacta. This refers to self-induced or self-aggravated, bizarre lesions without an obvious cause. ISN.

Generalized Morphea

Generalized morphea is a form of localized scleroderma. When morphea skin plaques are very widespread, it is referred to as generalized morphea. The skin patches become very hard and dark and spread over large areas of the body. Underlying muscles are often affected, causing them to tighten and atrophy. ISN.

Guttate Morphea

Guttate morphea may be a variant of lichen sclerosis and the two conditions can be seen in the same patient. It is characterized by small chalk white lesions that lack the firm center found in larger lesions of morphea. It involves primarily the neck and upper trunk areas of the body. American Osteopathic College of Dermatology.

Case Report: Patient with generalized guttate morphea and lichen sclerosus et atrophicus. Generalized guttate morphea is a very uncommon clinical entity. Clinically and histopathologically, they resembled lichen sclerosus et atrophicus. B. Blaya. (PubMed) Actas Dermosifiliogr.

Keloid Morphea

Keloid or Nodular Scleroderma. Sometimes keloids occur in patients who have scleroderma, and in particular they are more likely to occur in patients with systemic scleroderma. The terms "keloidal" or "nodular" scleroderma are used interchangeably. ISN.

Similar to Morphea: Morpheaform or Sclerosing Basal Cell Carcinoma

Morpheaform (sclerosing) (Figure 4). An indurated yellow-to-white plaque with an indistinct border and an atrophic surface characterizes morpheaform or sclerosing basal cell carcinoma (BCC). Ulceration and crusting are usually absent. This variety has an aggressive growth pattern and invasion of muscle, nerve, and bone may be seen. Morpheaform BCC is particularly insidious because of its benign scar-like appearance. Differential diagnosis of morpheaform BCC includes scar and localized superficial scleroderma (morphea). The Cleveland Clinic.

Morphea Profunda, also known as Subcutaneous Morphea

Case report: Extensive morphea profunda with autoantibodies and benign tumors. The term deep morphea describes a variant of morphea (localised scleroderma) in which inflammation and sclerosis are found in the deep dermis, panniculus, fascia or superficial muscle. Indian Dermatol Online J.

Subcutaneous morphea (Also known as morphea profunda) is noted by deep, bound-down, sclerotic plaques. This occurs much deeper in the skin and because of this the typical inflammatory changes and coloration is not generally seen. American Osteopathic College of Dermatology.

Primary Atrophic Solitary Morphea Profunda. Here, we describe a patient presenting with noninflammatory cupuliform (shaped like a small cup) depressed plaques, without any significant skin induration, pigmentation or texture change, that appeared on the left shoulder at a site of previous intramuscular vaccination. Our observation highlights the wide spectrum of clinical presentations of localized scleroderma. The latter should be considered in the presence of lipoatrophy-like lesions for proper workup and therapy. (Also see Causes of Scleroderma: Vaccinations and Lipodystrophy)

Personal Stories of Morphea Profunda

Tami: Morphea Scleroderma I have gotten used to the stares everyone casts my way because in their eyes I am different. Unique, I guess…

Terri: Subcutaneous Morphea I was finally diagnosed with deep morphea (or subcutaneous morphea) around mid February 2007, after having a biopsy…

Terry E. (Mojoy the Clown): Morphea Profunda Linear Scleroderma My right lower leg started to swell and the ankle grew big. It hurt all the time…

Pansclerotic Morphea

Pansclerotic Morphea is an exceedingly rare and severe form of morphea, which can be very disabling and sometimes even fatal. There are only a few reported cases of pansclerotic morphea in medical literature. ISN.

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